The Gorlin's syndrome: a case report.

نویسندگان

  • K C Ling
  • N T Couper
  • W S Hu
چکیده

Gorlin's syndrome, also known as multiple basal cell naevi syndrome, is a well documented disorder of unknown etiology. Very often it is familial of autosomal dominant mode of transmission. It can affect any age group of both sexes. rt presents a wide spectrum of signs and symptoms involving nearly every system of the body. Classically it consists of triad features of multiple basal cell naevi, jaw cysts and rib anomalies. However, many other associated defects had been reported, including calcification of falx cerebri, bridging of sella turcica,

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عنوان ژورنال:
  • The Medical journal of Malaysia

دوره 39 2  شماره 

صفحات  -

تاریخ انتشار 1984